Spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome.

PURPOSE: To describe a case of spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome, a disorder characterized by vascular fragility and associated severe bleeding problems.

METHODS

Observational case report. Spontaneous unilateral retrobulbar hemorrhage in a 22-year-old man with type IV Ehlers-Danlos syndrome was documented by clinical and radiographic examination.

RESULTS

The retrobulbar hemorrhage was self-limited and resolved without visual sequelae.

CONCLUSION

Spontaneous retrobulbar hemorrhage should be recognized as part of the spectrum of type IV Ehlers-Danlos syndrome, and clinicians must be alert to diagnosis and treatment of this vision-threatening problem.