A menopausal woman with mullerian agenesis, a leiomyoma, an inguinal hernia, and cystadenofibromas.

BACKGROUND

Müllerian agenesis, the second most common cause of primary amenorrhea, affects 1 in 4,000 to 10,000 women. Although the majority of these women have complete absence of the uterus, a small percentage can have a rudimentary uterus.

CASE: A menopausal nulligravida with known müllerian agenesis developed a large pelvic mass and an inguinal hernia. The patient underwent an exploratory laparotomy, which revealed a large leiomyoma growing from a small rudimentary uterus, an indirect inguinal hernia, and bilateral benign serous cystadenofibroma.

CONCLUSION

Women with müllerian agenesis and rudimentary uteri can develop gynecologic pathology similar to women with normal genital tracts.