[Solitary pelvic kidney and vaginal agenesia].

OBJECTIVE

To present a case of solitary pelvic kidney with congenital absence of the vagina.

METHODS

A patient with solitary pelvic kidney and vaginal aplasia is described. Patient evaluation included hematological, hormonal, cytogenetic, laparoscopic and imaging studies.

RESULTS

Blood, hormone and cytogenetic studies were normal. Laparoscopy showed absence of the uterus and both tubes and ovaries, which was confirmed by pneumopyelography. IVP showed absence of renal shadows and a solitary pelvic kidney.

CONCLUSIONS

Congenital absence of the vagina should be suspected in a patient with a pelvic solitary kidney consulting for primary amenorrhea.