Simultaneous aortic valve and arch replacement with bilateral nephrectomy for massive polycystic kidney disease, aortic regurgitation and dissecting aneurysm.

Aneurysmal dissection of the ascending aorta and arch may be associated with polycystic kidney disease. We report a case of massive polycystic kidneys leading to respiratory and gastrointestinal embarrassment in combination with aneurysmal dilatation of a chronic arch dissection managed by simultaneous bilateral nephrectomy and arch replacement.