The Ehlers-Danlos syndrome, type IV, with an unusual combination of organ malformations.

A patient having type IV Ehlers-Danlos syndrome is described because of an uncommon combination of malformations. He had multiple aneurysms, a hepatic artery-to-portal vein fistula, and diverticula of the biliary passages, the sigmoid colon, and bladder. He also suffered from scoliosis and dilatation of inner and outer cerebral spinal fluid containing spaces.