Oral surgery, oral medicine, oral pathology and oral radiology · 2013
Dentomaxillofacial manifestations of mucopolysaccharidosis VI: clinical and imaging findings from two cases, with an emphasis on the temporomandibular joint.
Клинический случайСтатьяНазвание и аннотация: Перевод в очереди
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Cavaleiro Rosely Maria dos Santos, Pinheiro Maria das G Rodrigues, Pinheiro Lucas R, Tuji Fabrício Mesquita, Feio Patrícia do Socorro Queiróz, de Souza Isabel Cristina Neves, Feio Raimunda Helena Ferreira, de Almeida Sâmia Cordovil, Schwartz Ida Vanessa Doederlein, Giugliani Roberto, Pinheiro João J V, Santana-da-Silva Luiz Carlos
Аннотация
OBJECTIVES: Using a clinical survey, panoramic, cone-beam computed tomography (CBCT), and magnetic resonance (MR) imaging, this study was conducted to ascertain primary maxillofacial abnormalities in patients with mucopolysaccharidosis VI (MPS VI).
STUDY DESIGN: Two patients previously diagnosed with MPS VI underwent clinical and imaging surveys (panoramic radiographs, CBCT, and MR imaging).
RESULTS: Jaw involvement was present in all patients. The most prevalent findings were enlarged marrow spaces, osteopenia, dentigerous cyst-like follicles, effacement of the jaw structures, and osteosclerosis. This is the first study to describe temporomandibular joint (TMJ) involvement for MPS VI.
CONCLUSIONS: CBCT and MR imaging were needed to observe features that were not clear in conventional radiographs. Both patients reported symptoms in the TMJ and demonstrated involvement during their examinations. A multicenter study is necessary to better document maxillofacial involvement in MPS VI.
STUDY DESIGN: Two patients previously diagnosed with MPS VI underwent clinical and imaging surveys (panoramic radiographs, CBCT, and MR imaging).
RESULTS: Jaw involvement was present in all patients. The most prevalent findings were enlarged marrow spaces, osteopenia, dentigerous cyst-like follicles, effacement of the jaw structures, and osteosclerosis. This is the first study to describe temporomandibular joint (TMJ) involvement for MPS VI.
CONCLUSIONS: CBCT and MR imaging were needed to observe features that were not clear in conventional radiographs. Both patients reported symptoms in the TMJ and demonstrated involvement during their examinations. A multicenter study is necessary to better document maxillofacial involvement in MPS VI.
Предметные рубрики MeSH
AdolescentBone Demineralization, PathologicBone Diseases, MetabolicBone MarrowCone-Beam Computed TomographyDental SacDentigerous CystFemaleFollow-Up StudiesHumansJaw DiseasesMagnetic Resonance ImagingMandibular DiseasesMaxillary SinusMucopolysaccharidosis IVNasal CavityOsteosclerosisPedigreeRadiography, PanoramicRoot ResorptionTemporomandibular Joint DisordersTooth DiseasesTooth, Impacted