Placental sulfatase deficiency and congenital ichthyosis with intrauterine fetal death: case report.

Placental sulfatase deficiency and congenital ichthyosis are two manifestations of an X-linked recessive inborn error of metabolism. This uncommon disorder can be diagnosed antenatally by maternal urinary steroid assays. A case with an affected sibling is presented, and the disorder's association with fetal death and failure to induce labor is discussed.