[A rare and little-known form of hypospadias].

A case of a 2-year-old boy with a rare form of hypospadia is reported. The anomaly consisted of the absence of a part of the urethral stem along 1.6 cm. The defect was filled with urethral mucosa instead of the testicular skin. The penis was not deformed. The foreskin was hooded. The defect was identified as segmentary urethral hypoplasia. This is a rare variant of hypospadia in which the urethral defect is repaired not with the skin but the mucosa.