Multicystic dysplastic disease of kidney in fetus.

Multicystic kidney disease remains the commonest cause of abnormally enlarged kidney, diagnosed on antenatal ultrasound examination. It is typically a unilateral disorder; bilateral condition is incompatible with extra uterine life. Survival is associated with higher risk ofWilm's tumor and Renal cell carcinoma. Diagnosis is facilitated by ultrasonography. Respiratory compromise on account of mass effect may need repeated percutaneous cyst aspiration. Nephrectomy is the definitive treatment option.