A unique case of descending salpingitis and functioning endometrium in a Müllerian remnant in a woman with Mayer-Rokitansky-Küster-Hauser syndrome.

OBJECTIVE

To describe a unique case of descending salpingitis and functioning endometrium in a noncavitated mullerian remnant in a patient with Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome.

DESIGN

Case report.

SETTING

Second Department of Obstetrics and Gynecology, University of Athens, Aretaieion Hospital, Athens, Greece.

PATIENT(S): A 25-year-old patient with MRKH syndrome who presented with lower abdominal pain.

INTERVENTION(S): Clinical examination, transabdominal ultrasonography, laparoscopy, laparotomy.

MAIN OUTCOME MEASURE(S): Clinical symptoms of salpingitis and hematometra; laparoscopic and laboratory confirmation.

RESULT(S): Laparoscopy revealed an infection of the right salpinx, and surgical excision by laparotomy revealed a noncanalized mullerian remnant with functioning endometrium.

CONCLUSION(S): Salpingitis can present in patients with MRKH syndrome. Probable presence of functioning endometrium must be taken under consideration.