Congenital cystic adenomatoid malformation type 0-a rare cause of neonatal death.

OBJECTIVE

We give the first account of failure of extracorporeal membrane oxygenation therapy secondary to congenital cystic malformation of the lung (CCAM) type 0.

DESIGN

Case report.

SETTING

Pediatric intensive care unit.

PATIENT: A female neonate, appropriate for gestational age, with respiratory failure immediately after delivery.

INTERVENTIONS: : Cardiopulmonary support with venoarterial extracorporeal membrane oxygenation.

RESULTS

There was no improvement of pulmonary function, and the patient died. CCAM type 0 was diagnosed postmortem.

CONCLUSIONS

CCAM type 0 should be considered as a rare differential diagnosis of irreversible lung pathologies leading to failure of extracorporeal membrane oxygenation therapy for neonatal respiratory failure.