Managing Acute Exacerbations in Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in the Intensive Care Unit Setting.

Idiopathic pulmonary fibrosis and progressive pulmonary fibrosis are advanced interstitial lung diseases with high morbidity and mortality, particularly during and following acute exacerbations. Intensive care unit admissions are often due to respiratory failure, with limited treatment options. Advanced life support measures, such as mechanical ventilation and extracorporeal membrane oxygenation, should be considered only as bridges to lung transplantation. The integration of palliative care and ongoing discussions about goals of care with patients and their families remain essential in managing these complex cases.