Left ventricular noncompaction - a case report.

Left Ventricular (LV) noncompaction is a rare disorder of endomyocardial morphogenesis. It has got a high mortality rate. It is frequently missed during diagnosis because of lack of suspicion and lack of definite diagnostic criteria. We are reporting a case of LV noncompaction in a Bangladeshi patient. Patient presented to us with history of repeated syncope. She had family history of sudden cardiac death. Clinically, there had a systolic murmur in left parasternal area. Her ECG showed different arrhythmia like atrial fibrillation, sinus bradycardia and Ventricular tachycardia. Her echocardiography showed features consistent with 'left ventricular noncompaction'. This is the first case report of this type in a Bangladeshi patient.