Severe scleritis and urticarial lesions.

PURPOSE: To report the first known case of bilateral scleritis in a patient with hypocomplementemic urticarial vasculitis.

DESIGN

Interventional case report.

METHODS

Medical and ophthalmic history, results of physical and ophthalmic examinations, laboratory data, and histologic and immunopathologic examination were reviewed and results recorded.

RESULTS

A 67-year-old man who presented with eye redness and pain, rash, arthralgia, and malaise was found to have hypocomplementemic urticarial vasculitis. Treatment with high-dose oral corticosteroids and mycophenolate mofetil resulted in the resolution of the rash and scleritis.

CONCLUSIONS

Ocular involvement may be a helpful clue in the diagnosis of this uncommon syndrome.