[COGAN SYNDROME - CASE PRESENTATION WITH PROGRESSIVE OCULAR INVOLVEMENT].

A 74-year-old female patient suffering from Cogan's syndrome, presented to our department with slow progression bilateral corneal clouding, leading to reduced vision in her right eye. Recently, the patient underwent combined surgery of penetrating keratoplasty with cataract extraction, which improved her vision significantly. Cogan syndrome is a rare progressive systemic disease with potentially severe visual impairment. Disease diagnosis is challenging and is conducted by exclusion. Patients can benefit from keratoplasty in progressive disease manifestation.