Hypoplastic Posterior Leaflet Mitral Valve Associated with Bicuspid Aortic Valve.

• Hypoplasia of the MV posterior leaflet is a rare congenital anomaly. • Differential diagnosis includes other anomalies of the mitral apparatus. • TTE and TEE are cornerstones for proper preoperative planning. • HPMVL tends to be incompatible with life. • Association of HPMVL with a BAV is extraordinarily rare.