Report of a rare case of childhood adrenocortical carcinoma and literature review.

Adrenocortical carcinoma (ACC)in children is rare, and its nonspecific clinical presentation renders early diagnosis challenging. Surgery remains the primary therapeutic approach. A multidisciplinary, multimodal treatment strategy and long-term follow-up are essential to improve prognosis. A retrospective analysis was conducted on the clinical data of a child diagnosed with ACC at our hospital, including symptoms, signs, imaging findings, surgical procedures, pathological results, and postoperative follow-up, We also perform a literature review to increase disease awareness and provide references for similar clinical cases in the future.