Rinsho shinkeigaku = Clinical neurology · 2017
[Adult-onset neuronal intranuclear inclusion disease presented transient global amnesia-a case report].
Клинический случайСтатьяНазвание и аннотация: Перевод пока не подготовлен
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Takeshita Jun, Kobayashi Hiromitsu, Shimoe Yutaka, Sone Jun, Sobue Gen, Kuriyama Masaru
Аннотация
A 65-year-old man had a transient amnesia for about 3 hours. Similar symptoms appeared three years ago. He did not manifest dementia, cerebellar ataxia and involuntary movements. Peripheral neuropathy was observed by the neurophysiological examinations. Diffusion weighted image showed high intensity signal in the area of the corticomedullary junction of the frontal to parietal lobes and immunohistochemical studies of biopsied skin revealed many intranuclear inclusion bodies. Adult-onset neuronal intranuclear inclusion disease was diagnosed. As there was no similar member in his family, he was a sporadic case. Clinical characteristics of his amnesia was fulfilled with the criteria of transient global amnesia (TGA). The transient disturbance of limbic system was suspected.