Congenital conjunctivo-limbo-corneal choristoma associated with marginal keratopathy.

We report a case of a three day old African baby who presented with a three day history of injected right eye. Examination disclosed an injected conjunctivo-limbo-corneal choristoma with associated marginal keratitis. Investigation disclosed a high maternal titer of rubella antibodies. The marginal lesions responded well to topical corticosteroids. Clinical manifestations of ocular choristomas epidemiology, classification, pathogenesis and indications for surgical treatment are discussed. We assume that an embryological error was the cause for the development of the choristomatous lesion but we cannot exclude the possibility of occult rubella infection during the early stages of pregnancy.