Cochlear Implantation for Rudimentary Otocysts: Two Case Reports.

OBJECTIVE

Rudimentary otocyst (RO) is characterized by an otic capsule without an internal auditory canal, which is considered a contraindication to cochlear implantation (CI). In this study, we were the first to report two patients with ROs who underwent CI.

PATIENT: Two patients (18 months old and 2 years old) presenting with bilateral congenital hearing loss were diagnosed with ROs.

INTERVENTION: CI was performed. The transmastoid slotted labyrinthotomy approach was used with customized MED-EL electrode arrays.

MAIN OUTCOME MEASURES: Categorical auditory performance, infant-toddler meaningful auditory integration of sound, the speech intelligibility rating, and meaningful use of speech scale.

RESULTS

Both children could understand common phrases and had intelligible, connected speech 2 years after CI.

CONCLUSION

With proper indication, surgical approach and postoperative training, a child with an RO may benefit from CI.