A Rare Intracardiac Manifestation of an Aggressive Malignant Peripheral Nerve Sheath Tumor in a Young Adult.

• A rare intracardiac metastasis from an MPNST was identified. • Multimodality imaging distinguished tumor from thrombus in the right ventricle. • CMR findings confirmed vascular neoplasm with late gadolinium enhancement. • This case shows the value of early echocardiography and CMR in high-risk sarcomas. • An interdisciplinary imaging approach guided management and prognosis.