Neurofibromatosis type 2: The future holds hope.

Progress in molecular biology has provided us with new understanding of neurofibromatosis type 2. The diagnosis of the condition is based on a number of clinical and radiological findings, which include the use of the scanner and MRI. The treatment objective is to preserve neurological function for as long as possible, with a minimum of surgical intervention. The dilemma is particularly great as far as the hearing is concerned. The care of these patients and their families must be carried out in highly specialised multi-disciplinary centres which have available the services of neuro-otologists, neurosurgeons, geneticists, audiologists, ophthalmologists and dermatologists.