[Histological examination of the human retina with congenital stationary night blindness].

We report histological findings of the retina from an eye with congenital stationary night blindness. The case was an 82-year-old woman who showed a Schubert-Bornschein type electroretinogram, and whose eye was enucleated due to orbital invasion of paranasal malignant melanoma. The retina had a disorganized outer plexiform layer with displaced nuclei of the outer and inner nuclear layer. There was also outward displacement of the cone nuclei, formation of hyaline and serous drusen, and disorganized retinal pigment epithelium as the histological changes due to aging. The histological abnormality seen in the outer nuclear layer could be responsible for the electrophysiological abnormality in this case.