[A case of meningioangiomatosis in an infant].

We report here a rare case of meningioangiomatosis in an infant, not associated with von Recklinghausen's disease. A 14-month-old female was admitted because of seizures. Neurological findings on admission were normal. Computed tomography showed a slightly high density mass with marked contrast enhancement in the left temporoparietal lobe. Magnetic resonance image (MRI) revealed a slightly hypointensive lesion surrounded by an isointensive band on T1-weighted image, and a hyperintensive lesion surrounded by a slightly hypointensive band on T2-weighted image. Brain edema was shown to a certain extent around the lesion on MRI. Left carotid angiography demonstrated a slightly upward shift of the left middle cerebral artery, but no abnormal vascularity was shown. A temporoparietal craniotomy was performed. A yellowish red, elastic soft tumor was observed in the left temporal lobe. The tumor resembled hyperemic hypertrophic gyri and was well demarcated. Total removal of the tumor was performed. Pathological diagnosis was meningioangiomatosis. The patient is still doing well 3 years and 5 months after the operation. There was no evidence of recurrence on computed tomography at the 3-year follow up. She didn't have any stigmata, such as café au lait spots or neurofibromas suggesting von Recklinghausen's disease.