Acta medica academica · 2025
Lodder-Merla Syndrome, a Multisystemic Disorder: Perioperative Anesthetic Management of an Infant.
СтатьяКлинический случайНазвание и аннотация: Перевод пока не подготовлен
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Astyrakaki Elsa, Garini Eleanna, Georgousi Savva, Tsitoura Dimitra, Gazelopoulou Eirini
Аннотация
OBJECTIVE: This paper aims to present the perioperative anesthetic challenges in an infant with Lodder-Merla syndrome.
CASE REPORT: We present a case report of a 7-month-old infant with Lodder-Merla syndrome, a pacemaker, epileptic spasms, and severe reflux, who was scheduled for open gastrostomy and gastrojejunal tube insertion. Such an intervention would constitute a second consecutive procedure under general anesthesia, shortly after pacemaker implantation. Perioperatively, emphasis was given to maintaining respiratory and cardiac stability, avoiding drugs with parasympathomimetic effects, preventing aspiration, optimizing ventilation, and controlling seizures.
CONCLUSION: Since Lodder-Merla syndrome affects many organs, perioperative multidisciplinary collaboration and optimization of the affected systems are fundamental.
CASE REPORT: We present a case report of a 7-month-old infant with Lodder-Merla syndrome, a pacemaker, epileptic spasms, and severe reflux, who was scheduled for open gastrostomy and gastrojejunal tube insertion. Such an intervention would constitute a second consecutive procedure under general anesthesia, shortly after pacemaker implantation. Perioperatively, emphasis was given to maintaining respiratory and cardiac stability, avoiding drugs with parasympathomimetic effects, preventing aspiration, optimizing ventilation, and controlling seizures.
CONCLUSION: Since Lodder-Merla syndrome affects many organs, perioperative multidisciplinary collaboration and optimization of the affected systems are fundamental.