Retroperitoneal pheochromocytoma with thorax and bilateral neck chemodectoma in patients with multiorgan sarcoidosis.

A 37-year-old man with multiorgan sarcoidosis, hypertension, and abdominal mass on CT was referred to the nuclear medicine department. PET/CT with 68Ga DOTATATE demonstrated an increased uptake in the abdominal mass and in the mediastinum, neck (bilaterally), and right jugular foramen; low uptake was observed in hilar and groin lymph nodes. MRI revealed abnormal focal lesions, showing increased signal on T2-weighted fat-saturated images, marked contrast enhancement on T1-weighted gradient-echo images, and restricted diffusion in the same locations as on PET/CT. Patients underwent surgery of abdominal mass and right neck tumors, with histologic diagnosis consistent with extra-adrenal pheochromocytoma and neck chemodectoma.