MedElevator Войти в исследования
← Поиск публикаций

DOI 10.11406/rinketsu.65.90

Медицинская библиотека · [Rinsho ketsueki] The Japanese journal of clinical hematology · 2024

[Successful immunosuppressive therapy in female hemophilia A developing inhibitor after perioperative administration of factor VIII products].

Yamaguchi Maki, Takaki Yusuke, Yamasaki Yoshitaka, Oya Shuki, Nakamura Takayuki, Morishige Satoshi, Aoyama Kazutoshi, Mouri Fumihiko, Takase Ryuta, Matsuo Yoko, Osaki Koichi, Nagafuji Koji, Okamura Takashi

Клинический случайАннотация на английскомСтатьяПеревод пока не подготовлен

Аннотация

A 62-year-old woman was diagnosed as a hemophilia A carrier (factor VIII activity 35%) on preoperative examination of an ovarian tumor. A total of 35,600 units of recombinant factor VIII products was administered perioperatively. On postoperative day 95, a subcutaneous hematoma formed and immunosuppressive therapy with prednisolone was started based on an APTT of 66 seconds, factor VIII (FVIII) activity of 3%, and FVIII inhibitor of 1 BU/ml. During this treatment, the patient was hospitalized due to ankle joint bleeds and required hemostatic treatment, but the inhibitor disappeared and FVIII activity recovered to 30% after postoperative day 438 with cyclophosphamide. F8 analysis revealed the patient carried a heterozygosity of p.Arg391Cys, which has previously been categorized as cross-reacting material (CRM)-positive severe hemophilia A. No high-risk mutations for inhibitor development were found. We also report the results of a desmopressin acetate hydrate test administered to the patient to prepare for future treatment in case of hemorrhage, since high-dose FVIII administration may have been a factor in inhibitor development.

Для цитирования: Yamaguchi Maki, Takaki Yusuke, Yamasaki Yoshitaka, Oya Shuki, Nakamura Takayuki, Morishige Satoshi, Aoyama Kazutoshi, Mouri Fumihiko, Takase Ryuta, Matsuo Yoko, Osaki Koichi, Nagafuji Koji, Okamura Takashi. [Successful immunosuppressive therapy in female hemophilia A developing inhibitor after perioperative administration of factor VIII products].. [Rinsho ketsueki] The Japanese journal of clinical hematology. 2024. DOI: 10.11406/rinketsu.65.90.

Предметные рубрики MeSH

Подготовка и перевод публикации
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…

История · было → стало

Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.

Тип публикации указан по данным источника. Уровень доказательности автоматически не присваивается.