Pure cheiro-oral syndrome due to a small pontine hematoma: report of a case and review of the literature.

Cheiro-oral syndrome is frequently associated with other neurologic deficits; its pure form is rare. We report a 60-year-old man with pure cheiro-oral syndrome due to a small hematoma located in the ventral tegmentum of the right upper pons. His sensory disturbance remained unchanged during a follow-up period of 16 months. Review of the literature suggests that the pons is the most frequent site of lesions in pure cheiro-oral syndrome.