Orbital Paraganglioma and Succinate Dehydrogenase Staining for Genetic Testing Triage and Prognosis.

PURPOSE OF THE STUDY: To describe the rare occurrence of a paraganglioma in the orbit and how to triage for genetic testing and assess the prognosis with succinate dehydrogenase subunit B (SDHB) immunohistochemical staining.

METHOD: Case report.

PROCEDURES: A 47-year-old 'Работает' male presented with painless exophthalmos and diplopia secondary to an infraorbital tumour mass.

RESULTS

The orbital biopsy was diagnosed as paraganglioma with positive staining with SDHB.

CONCLUSION

The rarity of an orbital paraganglioma was followed by the clinical search for a possible occult extraorbital primary paraganglioma. SDHB staining helped in the triage for genetic testing and gave an idea about the prognosis for this tumour.