A case report on cystic meningioma in cerebellopontine angle and recommendations for management.

RATIONALE: Cystic meningioma located at the cerebellopontine angle (CPA) is an extremely rare occurrence. It is frequently misdiagnosed preoperatively. Little is known about the clinical features and outcome of this rare disease.

PATIENT CONCERNS: A 70-year-old male presenting with progressive headache and gait disturbance.

DIAGNOSIS: According to the symptoms, signs, and Gd-enhanced magnetic resonance images (MRI), a preoperative diagnosis of hemangioblastoma located in left CPA was made. Finally, the histological examination revealed a meningioma.

INTERVENTIONS: A complete resection, including the part of the solid mass together with cyst, was performed.

OUTCOMES: The postoperative course of the patient was uneventful, and no residual or recurrent tumor was found during the 24-month follow-up period.

LESSONS: Cystic meningioma should be included in the differential diagnosis of a CPA mass with atypical radiologic features, such as a large cyst and enhanced mural nodule. By summarizing the related literature, we found that the most common pathological subtype of CPA cystic meningioma is the clear cell subtype, which belongs to WHO grade II. Gross total resection including the enhanced cyst wall is extremely important. A close follow-up is necessary because of the high recurrence rate in this subset of meningioma.