Giant cell tumor of the orbital roof: A case report and brief review of literature.

Giant cell tumors (GCTs) of bone are rare, locally aggressive primary neoplasms that account for approximately 3%-7% of all primary bone tumors. They most commonly arise in the epiphyses of long bones in young adults and are seldom seen in the craniofacial skeleton. Involvement of the frontal bone with orbital extension is exceptionally rare, particularly in the pediatric age group. We report a case of a 9-year-old male who presented with a progressively enlarging swelling of the left orbit associated with vision loss with atypical imaging features and an intracranial component with compression of the adjacent brain parenchyma. Histopathological examination subsequently confirmed the diagnosis of GCT. He was managed with a multimodal approach comprising neoadjuvant therapy and surgical excision, which achieved complete tumor removal, with no evidence of recurrence at 1-year follow-up. This case highlights the need for awareness of rare sites of presentation of GCT and the importance of considering it in the differential diagnosis of destructive calvarial masses with orbital involvement in children.