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DOI 10.7181/acfs.2022.01067

Медицинская библиотека · Archives of craniofacial surgery · 2023

Lymphaticovenular anastomosis for Morbihan disease: a case report.

Hong Jung Hyun, Yi Changryul Claud, Lee Jae Woo, Bae Yong Chan, Kim Ryuck Seong, Kim Joo Hyoung

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Аннотация

Morbihan disease (MD) is a very rare condition characterized by rosaceous or erythematous lymphedema on the upper twothirds of the face. A definitive management strategy for MD is lacking, and treatment is challenging. Herein, we present a case of persistent bilateral eyelid edema treated by lymphaticovenular anastomosis (LVA) and lymph node-vein bypass surgery. The patient experienced persistent bilateral eyelid edema. Indocyanine green lymphography was performed, and the diagnosis of bilateral facial lymphedema was confirmed. On the right side, a preauricular lymphatic vessel was anastomosed to a vein. On the left side, lymphostomy on the preauricular lymph node was done, with anastomosis to the transected proximal end of the concomitant vein of the transverse facial artery. Furthermore, a preauricular lymphatic vessel was anastomosed to a vein. Eyelid edema decreased and progressively improved on both sides. The outcome of this case suggests that LVA and lymph node-vein bypass surgery are appropriate for treating persistent eyelid edema related to MD.

Для цитирования: Hong Jung Hyun, Yi Changryul Claud, Lee Jae Woo, Bae Yong Chan, Kim Ryuck Seong, Kim Joo Hyoung. Lymphaticovenular anastomosis for Morbihan disease: a case report.. Archives of craniofacial surgery. 2023. DOI: 10.7181/acfs.2022.01067.
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