Generalized odontodysplasia concomitant with mild hypophosphatasia--a case report.

An abnormal exfoliation pattern of the primary teeth is a sign of a systemic abnormality affecting more than just the oral structures. A prompt investigation of the cause of this condition is mandatory to identify any disease process and to initiate the required treatment. This article presents a case of mild hypophosphatasia concomitant with odontodysplasia in a 4 1/2-year-old female. The child's condition was first detected due to the early exfoliation of her primary teeth. This article also discusses the two different disease entities and the reasoning that led to the final diagnosis.