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Медицинская библиотека · Annali italiani di chirurgia · 2023

Laparoscopic adrenalectomy for giant pheochromocytoma. What is the size limit ?

Di Nuzzo Maria Michela, Castiglioni Simone, Pirozzi Nello, Di Santo Albini Andrea Gianmario, De Luca Marcello, Tedesco Anna, Bardascino Francesca, de Werra Carlo, Corcione Francesco

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Аннотация

AIM: This case report describes a giant pheochromocytoma in a young female, experienced cardiac symptoms, treated by a transperitoneal laparoscopic right adrenalectomy.

MATERIAL AND

METHODS

A 29 years old female with Taki-tsubo syndrome, consequent to the chronic release of catecholamines, with a palpable abdominal mass and vague abdominal symptoms was referred to our department. Abdominal CT scan has demonstrated a solid mass of 13 cm in the right adrenal space so, after pre-operative management with alpha-adrenergic receptor and beta blockade and a 3D CT scan reconstruction a right adrenalectomy laparoscopic approach was performed.

RESULTS

Our result underlines that 13 cm in size for a giant pheochromocytoma is not an absolute contraindication to perform a minimally invasive approach in expert hands, with optimal surgical, oncological and cosmetic results.

DISCUSSION: The only curative option for non-metastatic pheochromocytomas disease is surgical resection. Laparoscopic adrenalectomy is the treatment of choice but the limit size for a safe and feasible minimally invasive approach is not yet defined.

CONCLUSIONS

This case report could help to better define more solid recommendations in the next future and also provide landmarks and key steps for laparoscopic surgeons.

KEY WORDS: Giant Pheochromocytoma, Laparoscopic Adrenalectomy, Pheochromocytoma Management.

Для цитирования: Di Nuzzo Maria Michela, Castiglioni Simone, Pirozzi Nello, Di Santo Albini Andrea Gianmario, De Luca Marcello, Tedesco Anna, Bardascino Francesca, de Werra Carlo, Corcione Francesco. Laparoscopic adrenalectomy for giant pheochromocytoma. What is the size limit ?. Annali italiani di chirurgia. 2023.

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