[The clinical manifestation and management of Mondini dysplasia].

OBJECTIVE

To improve the possibility of diagnosis of the Mondini dysplasia.

METHOD: The clinical manifestation and the examination of CT and MRI and surgical treatment of the Mondini dysplasia were discussed.

RESULT: Because Mondini dysplasia with cerebrospinal fluid leak would occur recurrent meningitis, the patients were often difficult to be diagnosed. Especially. if the defect was unilateral, it was frequently unrecognized.

CONCLUSION

The patients with recurrently unclear cerebrospinal fluid leak and meningitis would be suspected. The diagnosis of the disease is based on the examination of the temporal bone CT and MRI. To the patients with cerebrospinal fluid leak, a transtympanic closure is one of very effective management.