Concentric Stenting of the Right Ventricular Outflow Tract in Complex Multilevel Obstruction.

BACKGROUND

Tetralogy of Fallot (TOF) with pulmonary atresia and major aortopulmonary collateral arteries (MAPCAs) presents significant challenges in management in the presence of right ventricular (RV) hypertension secondary to multilevel right ventricular outflow tract (RVOT) obstruction.

CASE SUMMARY: A 5-month-old boy with a history of TOF, pulmonary atresia, and MAPCAs who underwent MAPCA unifocalization and TOF repair presented with suprasystemic RV pressures. Diagnostic catheterization showed severe RVOT obstruction at the conduit insertion site owing to the presence of concentric muscle bundles, which was treated with overlapping bare metal stents given his high-risk surgical candidacy.

DISCUSSION: Stent fracture is a recognized complication; however, this case demonstrates that concentric stenting can effectively relieve RVOT obstruction in patients who are not surgical candidates.

TAKE-HOME MESSAGE: Concentric stenting of the RVOT is a viable option for managing complex RVOT obstruction in pediatric patients with congenital heart disease who are not surgical candidates.