Lymphangiosarcoma of the jejunum in a 44-year-old man: report of a case and review of literature.

Lymphangiosarcoma is a malignant tumor arising from lymphatic endothelial cells and has largely been abandoned in the current classification of endothelial neoplasms. Recently, lymphangiosarcoma has been resurrected by several novel markers for lymphatic endothelium available for immunohistochemistry. Here, we reported a new case of lymphangiosarcoma that was located in the Jejunum of a 44-year-old man. To our best knowledge, this is the first report of lymphangiosarcoma in small intestine with no known history of lymphedema, lymphaticmalformation or previous radiation.