Rare case of complicated congenital anomalies of female reproductive organs with bilateral undescended ovaries.

Congenital anomalies of the female reproductive organs vary widely and the patients often have no symptoms related to them. We report an exceedingly rare case of complicated anomalies in the Müllerian duct and urogenital sinus. The patient was a 21-year-old woman evaluated for infertility, and the examination revealed the presence of a complete septate uterus. We found dual vaginal canals with right incomplete hymenal fenestration when we performed an examination during the patient's menstrual period. Laparoscopic findings showed bilateral undescended ovaries, absent utero-ovarian ligaments, and partial atresia of the left fallopian tube. We performed hymenotomy of the right vagina, resection of the vaginal septum and salpingostomy of the left fallopian tube. To the best of our knowledge, this is the first report to describe this complex combination of anomalies in the Müllerian duct and urogenital sinus. This case might provide us with information about the development of the female reproductive organs. © 2016 Japan Society of Obstetrics and Gynecology.