Internal medicine (Tokyo, Japan) · 2018
Suspected Hepatically Localized Granulomatosis with Polyangiitis.
Клинический случайСтатьяНазвание и аннотация: Перевод пока не подготовлен
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Yamamoto Toshiki, Ryuzaki Hitomi, Kobayashi Shun, Ohshiro Shu, Ogawa Masahiro, Tanaka Naohide, Gotoda Takuji, Moriyama Mitsuhiko, Kinukawa Noriko, Sugitani Masahiko, Notohara Kenji
Аннотация
The patient was a 72-year-old woman whose alkaline phosphatase levels had been elevated since she was 56 years old. Liver biopsies obtained when the patient was 64 and 66 years of age led to a suspicion of cholangitis caused by vasculitis. Furthermore, proteinase-3 anti-neutrophil cytoplasmic antibody positivity led to a suspicion of granulomatosis with polyangiitis, but subjective symptoms and disorders in other organs were absent, so this suspicion was not confirmed. Cholangitis caused by vasculitis rarely occurs without vasculitis in other organs. We herein report this case in which we obtained distinctive laparoscopic and imaging findings that raised suspicions of liver circulatory failure.