Malignant non-teratoid medulloepithelioma with submandibular metastases.

Medulloepithelioma is a tumor of the primitive medullary epithelium overlying the ciliary body. Most become evident early in life, and they may be malignant, although distant metastases are rare. The purpose of this report is to describe a malignant nonteratoid neoplasm and its metastasis to the submandibular lymph nodes and to introduce this uncommon neoplasm with otolaryngologists.