Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery · 2018
Rapidly progressive fatal idiopathic hypertrophic pachymeningitis with brainstem involvement in a child.
Клинический случайСтатьяНазвание и аннотация: Перевод пока не подготовлен
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Tsuchida Kosuke, Fukumura Shinobu, Yamamoto Akiyo, Akiyama Yukinori, Hirano Hiroshi, Tsutsumi Hiroyuki
Аннотация
BACKGROUND: Hypertrophic pachymeningitis (HP) is a rare disorder characterized by diffuse thickening of the dura mater with resultant neurologic deficits. HP develops secondary to various conditions or idiopathically usually in adults but rarely in children.
CASE REPORT: We describe a 3-year-old female child with idiopathic HP. Her HP involved the entire central nervous system with progression into the brainstem. The lesion responded poorly to pulsed steroids or any immunosuppressants. The brainstem lesion grew rapidly and formed various nodules that ultimately resulted in brain death. This is the first fatal case of HP in a child.
CASE REPORT: We describe a 3-year-old female child with idiopathic HP. Her HP involved the entire central nervous system with progression into the brainstem. The lesion responded poorly to pulsed steroids or any immunosuppressants. The brainstem lesion grew rapidly and formed various nodules that ultimately resulted in brain death. This is the first fatal case of HP in a child.