Cardiology in the young · 2026
Left pulmonary artery from the common carotid artery in DiGeorge syndrome: a case of ductal stenting as bridge to repair.
СтатьяКлинический случайНазвание и аннотация: Перевод пока не подготовлен
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
da Silva Lopes Manuela, Curinha Filipa, Dias João, Amaral Maria Emanuel, Silva Patrícia Vaz, Pires António
Аннотация
DiGeorge syndrome is associated with a wide spectrum of cardiovascular anomalies. We present a rare and anatomically complex arch anomaly in this context. A male newborn with prenatally diagnosed DiGeorge syndrome and a right aortic arch was suspected of having a left pulmonary artery arising from the ascending aorta. Postnatal multimodal imaging revealed a discontinuous left pulmonary artery originating anomalously from the left common carotid artery via a left-sided ductus arteriosus, which later developed significant stenosis. To preserve left pulmonary artery flow and promote its growth, percutaneous ductal stenting was successfully performed on day 33 of life, as a bridge to future surgical reimplantation. This case illustrates a rare embryological variant of pulmonary artery discontinuity. It highlights the diagnostic challenge from prenatal suspicion to postnatal definitive imaging, crucial for distinguishing this entity from a truly “absent” pulmonary artery and for planning appropriate intervention. The management underscores the role of hybrid palliation as a viable option to maintain pulmonary perfusion and enable delayed, safer surgical repair.