Case Report: Simultaneous repair of cerebrospinal fluid otorrhea and cochlear implantation in a patient with single-sided deafness and inner ear anomaly.

An-five years old male presented with recurrent attacks of headache and clear nasal discharge. Magnetic resonance cerebrospinal fluid (CSF) imaging demonstrated descent of the cerebellar tonsils, with CSF signal identified within the left middle ear. Temporal bone computed tomography showed the left cochlea was incomplete partition type I. Audiological evaluation revealed profound sensorineural hearing loss in the left ear of the pediatric patient. The surgical approach of mastoidotomy with exploration was utilized in the management of this pediatric case. CSF otorrhea was confirmed and the CSF leak was successfully localized at the oval window. The pediatric patient underwent repair of CSF otorrhea with concurrent cochlear implantation. Postoperatively, there was no recurrence of CSF otorrhea, and hearing was restored in the left ear. This report describes the first case of simultaneous repair of cerebrospinal fluid (CSF) otorrhea and cochlear implantation for the management of both CSF otorrhea and acquired unilateral profound sensorineural hearing loss.