Cutaneous mucormycosis in a patient with Hailey-Hailey disease (benign familial pemphigus) - first reported case.

This report describes a case of primary cutaneous mucormycosis in a patient with Hailey-Hailey Disease (benign familial pemphigus). The diagnosis of primary cutaneous mucormycosis was confirmed via microbiological culture as well as histopathology. Our patient improved with prompt surgical debridement and excision of infected, necrotic tissue with complementary antifungal therapy. To the best of our knowledge this is the first reported case of cutaneous mucormycosis in a patient with Hailey-Hailey Disease and contributes to the literature regarding pathophysiology, management and treatment for each of these rare entities.