Imperforate tricuspid valve with severe hypoplasia associated with an atypical vascular ring in the set of left isomerism. First case report.

Bodily isomerism, often referred to as "Heterotaxy," is the clinical entity in which the thoracic organs are themselves mirror-imaged in the same individual. The thoracic isomerism can be right or left. The left thoracic isomerism always has both atria with their atrial appendages of left morphology and frequently a mixed atrioventricular connection. Usually, there are two well-developed ventricles; however, in some cases, there may be univentricular physiology. In the set of left thoracic isomerism, no case of imperforate tricuspid valve with severe hypoplasia associated with a vascular ring has been reported in the literature.