Rare Presentation of Mucous Membrane Pemphigoid With Pemphigoid of the Pulmonary System in 10-Month-Old Female.

We present a 10-month-old girl with diffuse mucous membrane pemphigoid (MMP) and pemphigoid of the pulmonary system (POPS). Systemic corticosteroids, intravenous immunoglobulin, cyclophosphamide, rituximab, and mycophenolate mofetil led to improvement in cutaneous and mucosal lesions. However, she had progressively worsening airway involvement refractory to immunosuppression and ultimately died from respiratory failure.