[Hallervorden-Spatz disease].

Based on the history of a 5-year-old boy, the clinical picture and the natural history of Hallervorden-Spatz disease are reviewed. In the past, the diagnosis of Hallervorden-Spatz disease has usually been made only post mortem. In the T2 weighted MRI images "eye of the tiger" sign is seen. This is due to iron-accumulation in the pallidum and it makes the earlier, in vivo diagnosis of the disease possible.