An Unusual Case of a Vulva Tumor in an Adolescent: A Case Report and Literature Review.

BACKGROUND

We present the case of a 15-year-old adolescent with swelling in the left vulva that was found to have a tumor measuring approximately 20x15 cm in her vulva. Ewing's sarcoma/primitive neuroectodermal tumors (ES/PNET) are rare and malignant.

MATERIALS AND

METHODS

Preoperative magnetic resonance imaging and computed tomography performed to screen for metastasis were negative. The mass was surgically excised in total.

RESULTS

Immunohistochemistry showed the mass to be ES/PNET. The patient underwent positron emission tomography-computed tomography which revealed metastasis to inguinal lymph nodes and bone. While under chemotherapy for stage-4 ES/PNET, the patient was found to have lung metastasis. She died due to recurrent chemotherapy complications during treatment.

CONCLUSIONS

This rare case highlights that significant of early diagnosis and multidisciplinary approach to treatment of ES/PNET cases.