[Hallervorden-Spatz syndrome: report of a case].

It is reported the case of a male patient with 19 years old presenting progressive behavior disturbance and dystonic posture beginning on right, with approximately five years of evolution. Extrapyramidal and pyramidal syndrome was evidenced at examination. This finding suggests Hallervorden-Spatz disease which was confirmed by resonance imaging (MRI). The purpose of reporting this case is to call attention for the importance of MRI in the study of degenerative diseases of the nervous system.