Successful spinal anesthesia in a patient with mucopolysaccharidosis type I under femoral fracture reduction and external fixation.

INTRODUCTION

Mucopolysaccharidosis (MPS) is an inherited lysosomal storage disorders with glycosaminoglycans accumulation in tissues. MPS patients undergoing intratracheal intubation anesthesia show high mortality, with serious anesthetic complications associated with airway thickness and narrow. The regional anesthesia is a useful alternative to general anesthesia, however performing spinal anesthesia in MPS patients are rarely documented.

CASE PRESENTATION: We report a case of a boy with MPS type I undergoing femoral reduction and external fixation under spinal anesthesia in combination with sevoflurane inhalational induction, getting rid of difficulties associated with intubation.

CONCLUSION

Sevoflurane inhalational induction with spinal anesthesia without tracheal intubation is a safe choice for MPS I patient.